Aggravation of pseudomyxoma peritonei recognized 31 months post appendectomy

Hiromi Ono


Pseudomyxoma peritonei (PMP) is a rare type of peritoneal secondary tumor. Theincidence of PMP is approximately 1 per million population per year. A 63-year-old Japanese female was referred to our hospital with an acute appenditis. Abdominal computed tomography (CT) scan revealed a peripheral liver ascites. Appendectomy was performed on the same day. A low-grade appendiceal mucinous neoplasm was diagnosed pathologically. She returned to our hospital with an abdominal distention and fullness 31 months post appendectomy. Abdominal CT scan could view an ascites in pelvic cavity. An aggravation of PMP was recognized clinically. PMP is an interesting syndrome with unique clinical and pathologic challenges. Although predictions reveal that, most cases will arise from low-grade appendiceal mucinous lesions, it remains challenging to classify as an entity. Standard treatment is peritoneotomy and hyperthermic intraperitoneal chemotherapy. Then, it needs continued monitoring post appendectomy since the recurrence of PMP is common.


Hyperthermic intraperitoneal chemotherapy, Low-grade appendiceal mucinous neoplasm, Peritoneotomy, Pseudomyxoma peritonei


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